Pierre Robin Sequence: Review of Literature

Abstract

Pierre Robin sequence is a condition with the typical triad of micrognathia or retrognathia, cleft palate (classically U-shaped but V-shaped may occur usually without cleft lip and glossoptosis. Originally described by St Hilaire in 1822, Pierre Robins published a case of an infant with the condition in 1926. Pierre Robin Sequence is called a sequence because the underdeveloped lower jaw commences a sequence of events which leads to the abnormal displacement of the tongue and consequence formation of a cleft palate. The condition presents with bearing, respiratory and feeding problems. In this review, the historical background, aetiopathogenesis, clinical presentation and the evaluation of the condition are described. The various methods of treatment and the complications are also discussed.